A pediatric case of orbital inflammation and sinusitis- the diagnostic boundary between localized ANCA-associated vasculitis and IgG4-related disease. (PubMed, ARP Rheumatol) - Oct 12, 2026 - "Although glucocorticoid therapy initially achieved clinical improvement, relapses occurred, prompting treatment with rituximab. Treatment was intensified with mycophenolate mofetil and corticosteroids, resulting in remission. This case highlights the diagnostic and therapeutic challenges posed by overlapping features of AAV and IgG4-RD."
Journal • ANCA Vasculitis • Inflammation • Ocular Inflammation • Otorhinolaryngology • Pediatrics • Rare Diseases • Respiratory Diseases • Sinusitis • Vasculitis • MPO
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Ana Pestana Lopes; Carla Conceição; Inês Soares da Cunha; João Farela Neves; Manuela Mafra; Mara Ferreira; Marta Cabral; Marta Conde; Rita Luís; Rodrigo Cavalcanti; Vitória Cadete
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